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OBSTETRIC ANESTHESIOLOGY

Anesthetic Management of Seven Deliveries in Three Sisters with the May-Hegglin Anomaly

Eric B. Fishman, MD^*, Jean M. Connors, MD, and William R. Camann, MD

From the *Department of Anesthesiology, WellStar Kennestone Hospital, Marietta, Georgia; Division of Hematology, Department of Medicine, Harvard Medical School, Brigham and Women’s Hospital; and Department of Anesthesiology, Harvard Medical School, Brigham and Women’s Hospital, Boston, Massachusetts.

Address correspondence and reprint requests to Dr. William R. Camann, Department of Anesthesiology, Brigham and Women’s Hospital, 75 Francis St., Boston, MA 02115. Address e-mail to wcamann{at}partners.org.

Abstract

May-Hegglin anomaly is a rare genetic hematological disorder characterized by thrombocytopenia, but platelet function is usually normal. Three sisters with May-Hegglin anomaly and thrombocytopenia (platelet counts 14,000–100,000/mm³) were given neuraxial anesthesia for a total of 7 deliveries, 5 vaginal and 2 cesarean. None of the women had complications and no blood products were transfused.