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Anesth Analg 2004;98:68-69
© 2004 International Anesthesia Research Society

PEDIATRIC ANESTHESIA

Pyloromyotomy in a Patient with Paramyotonia Congenita

Binnaz Ay, MD*, Arzu Gerçek, MD*, Varlik I. Dogan, MD*, Gürsu Kiyan, MD{dagger}, and Yilmaz F. Gögüs, MD*

Departments of *Anesthesiology and Reanimation and {dagger}Pediatric Surgery, Marmara University Medical School, Istanbul, Turkey

Address correspondence and reprint requests to Dr. Arzu Gerçek, Yaliboyu c. Emanet s. Emek ap. No: 2/28 Bostanci 81110 Istanbul, Turkey. Address e-mail to agercek{at}hotmail.com

A 2-mo-old infant with paramyotonia congenita was scheduled for pyloromyotomy and repair of inguinal hernia. Diagnosis of paramyotonia congenita was done with positive family history, myotonia at eyelids, provocation by cold, and electromyogram analysis. Anesthesia was induced via face mask with sevoflurane at 4 minimum alveolar anesthetic concentration in oxygen. Tracheal intubation was attempted without a neuromuscular relaxant. Anesthesia was maintained with sevoflurane at 0.5 minimum alveolar anesthetic concentration in oxygen and remifentanil infusion at a rate of 0.2 µg · kg-1 · min-1. After discontinuation of sevoflurane and remifentanil, the patient was awake and had full recovery of muscle activity.

IMPLICATIONS: The literature concerning general anesthesia in paramyotonic patients is limited. We report a case of paramyotonia congenita in a 2-mo-old male infant undergoing surgery for pyloric stenosis and inguinal hernia after an uneventful anesthesia.




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[Abstract] [Full Text] [PDF]


Lippincott, Williams & Wilkins Anesthesia & Analgesia® is published for the International Anesthesia Research Society® by Lippincott Williams & Wilkins and Stanford University Libraries' HighWire Press®. Copyright 2004 by the International Anesthesia Research Society. Online ISSN: 1526-7598   Print ISSN: 0003-2999 HighWire Press
Copyright © 2004 by the International Anesthesia Research Society.